• Tel: 858.663.9055
  • SeparatorEmail: info@nsjbio.com
  • Tel: 858.663.9055
  • Email: info@nsjbio.com
Order
Home >> Antibodies >> GAA Antibody / Glucosidase alpha acid

GAA Antibody / Glucosidase alpha acid (F54279)

NSJ bio Image Pdf Image
  Catalog No Formulation Size Price (USD)  
Image F54279-0.4ML In 1X PBS, pH 7.4, with 0.09% sodium azide 0.4 ml 399
Image
F54279-0.08ML In 1X PBS, pH 7.4, with 0.09% sodium azide 0.08 ml 185
Bulk quote request
Western blot testing of human 1) HeLa, 2) MCF7, 3) SW620 and 4) A549 cell lysate with GAA antibody. Predicted molecular weight ~105 kDa.
›
Western blot testing of human 1) HeLa, 2) MCF7, 3) SW620 and 4) A549 cell lysate with GAA antibody. Predicted molecular weight ~105 kDa.
Western blot testing of human 1) A549, 2) MCF7, 3) SW620 and 4) PC-3 cell lysate with GAA antibody. Predicted molecular weight ~105 kDa.
Western blot testing of human placenta lysate with GAA antibody. Predicted molecular weight ~105 kDa.
IHC testing of FFPE human placenta tissue with GAA antibody. HIER: steam section in pH6 citrate buffer for 20 min and allow to cool prior to staining.
IHC testing of FFPE human liver tissue with GAA antibody. HIER: steam section in pH6 citrate buffer for 20 min and allow to cool prior to staining.
Availability 1-3 business days
Species Reactivity Human
Format Purified
Clonality Polyclonal (rabbit origin)
Isotype Rabbit Ig
Purity Antigen affinity purified
UniProt P10253
Applications Western blot : 1:500-1:2000
Immunohistochemistry (FFPE) : 1:25
Limitations This GAA antibody is available for research use only.
Review this product on BioCompare and get a $20 Amazon gift card

Related Products

Description

This gene encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Three transcript variants encoding the same protein have been found for this gene.

Application Notes

The stated application concentrations are suggested starting points. Titration of the GAA antibody may be required due to differences in protocols and secondary/substrate sensitivity.

Immunogen

A portion of amino acids 174-203 from the human protein were used as the immunogen for the GAA antibody.

Storage

Aliquot the GAA antibody and store frozen at -20oC or colder. Avoid repeated freeze-thaw cycles.

Related Products

   1.   View all GAA antibodies

Cross
Bulk Quote Request Form
Name*:
Organization*:
Email*:
Phone Number*:
Catalog No.*:
Comments and Specifics(amount, formulation, etc.)*:
Validation code: Captchapackage Image


Can't read the image? click here to refresh.
    *required field

Your bulk quote request has been submitted successfully!

Please contact us if you have any questions.